Tolosa Hunt Syndrome
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NORD is very grateful to Roman Shinder, MD, Assistant Professor of Ophthalmology, Ophthalmic Plastic & Reconstructive Surgery, SUNY Downstate Medical Center; Director Oculoplastics, Kings County Hospital Center and Renelle Pointdujour, MD, Department of Ophthalmology, SUNY Downstate Medical Center, for assistance in the preparation of this report.
Synonyms of Tolosa Hunt Syndrome
- ophthalmoplegia, painful
- ophthalmoplegia, recurrent
- ophthalmoplegia syndrome
- No subdivisions found.
Tolosa-Hunt syndrome is a rare disorder characterized by severe periorbital headaches, along with decreased and painful eye movements (ophthalmoplegia). Symptoms usually affect only one eye (unilateral). In most cases, affected individuals experience intense sharp pain and decreased eye movements. Symptoms often will subside without intervention (spontaneous remission) and may recur without a distinct pattern (randomly). Affected individuals may exhibit signs of paralysis (palsy) of certain cranial nerves such as drooping of the upper eyelid (ptosis), double vision (diplopia), large pupil, and facial numbness. The affected eye often abnormally protrudes (proptosis). The exact cause of Tolosa-Hunt syndrome is not known, but the disorder is thought to be associated with inflammation of specific areas behind the eye (cavernous sinus and superior orbital fissure).
Tolosa Hunt Syndrome Resources
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