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Locked In Syndrome

Abstract

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NORD is very grateful to Steven Laureys, MD, PhD, Coma Science Group, University Hospital of Liege, Belgium, for assistance in the preparation of this report.

Synonyms of Locked In Syndrome

  • cerebromedullospinal disconnection
  • de-efferented state
  • pseudocoma

Disorder Subdivisions

  • No subdivisions found.

General Discussion

Locked-in syndrome is a rare neurological disorder in which there is complete paralysis of all voluntary muscles except for the ones that control the movements of the eyes. Individuals with locked-in syndrome are conscious and awake, but have no ability to produce movements (outside of eye movement) or to speak (aphonia). Cognitive function is usually unaffected. Communication is possible through eye movements or blinking. Locked-in syndrome is caused by damaged to the pons, a part of the brainstem that contains nerve fibers that relay information to other areas of the brain.

Organizations related to Locked In Syndrome

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