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Budd Chiari Syndrome

Abstract

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Synonyms of Budd Chiari Syndrome

  • Budd's Syndrome
  • Chiari-Budd Syndrome
  • Chiari's Disease
  • Hepatic Veno-Occlusive Disease
  • Rokitansky's Disease

Disorder Subdivisions

  • No subdivisions found.

General Discussion

Budd-Chiari syndrome is a rare disorder characterized by narrowing and obstruction (occlusion) of the veins of the liver (hepatic veins). Symptoms associated with Budd Chiari syndrome include pain in the upper right part of the abdomen, an abnormally large liver (hepatomegaly), and/or accumulation of fluid in the space (peritoneal cavity) between the two layers of the membrane that lines the stomach (ascites). Additional findings that may be associated with the disorder include nausea, vomiting, and/or an abnormally large spleen (splenomegaly). The severity of the disorder varies from case to case, depending upon the site and number of affected veins. In some cases, if the major hepatic veins are involved, high blood pressure in the veins carrying blood from the gastrointestinal (GI) tract back to the heart through the liver (portal hypertension) may be present. In most cases, the exact cause of Budd-Chiari syndrome is unknown.

Budd Chiari Syndrome Resources

Organizations:

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