Amyopathic dermatomyositis

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Disease Overview

Amyopathic dermatomyositis is a form of dermatomyositis characterized by the presence of typical skin findings without muscle weakness.[5743][5744] Some of the skin changes that suggest dermatomyositis include a pink rash on the face, neck, forearms and upper chest; Gottron’s papules and heliotrope eyelids.[5744][5745][5746] Pruritis and photosensitivity are common, as is scalp inflammation and thinning of the hair.[5744][5745] While patients with amyopathic dermatomyositis should not have clinically evident muscle weakness, minor muscle abnormalities may be included. Fatigue is reported in at least 50% of patients.[5744] Some cases have been associated with internal malignancy and/or interstitial lung disease.[5747] Treatment may include sun avoidance, ample use of sunscreen, topical corticosteroids, antimalarial agents, methotrexate, mycophenolate mofetil, or intravenous (IV) immunoglobulin.[5743]


Synonyms

  • ADM
  • Dermatomyositis sine myositis

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National Organization for Rare Disorders