Dermatofibrosarcoma protuberans

Disease Overview

Dermatofibrosarcoma protuberans is an uncommon cancer in which tumors arise in the deeper layers of skin. The tumor usually starts as a small, firm patch of skin; it may be purplish, reddish, or flesh-colored. It is commonly found on the torso, usually in the shoulder and chest area. The tumor typically grows slowly but has a tendency to recur after being removed. It rarely spreads to other parts of the body. The cause of DFSP is unknown, but injury to the affected skin may be a predisposing factor. Treatment usually involves surgically removing the tumor. If the tumor is unable to be removed completely, additional therapy may be needed. Regular follow-up is important to monitor for recurrence.[10607][10608][10609]

Synonyms

• DFSP
• Giant cell fibroblastoma
• Familial dermatofibrosarcoma protuberans (subtype)
• Metastatic dermatofibrosarcoma protuberans (subtype)