Hemorrhagic shock and encephalopathy syndrome

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Disease Overview

Hemorrhagic shock and encephalopathy syndrome (HSES) is a rare disease that occurs suddenly in previously healthy children. This condition is characterized by severe shock, impairment of the blood’s ability to clot (coagulopathy), abnormal brain function or structure (encephalopathy), and liver and kidney dysfunction. Most cases of HSES occur in infants from age 3 to 8 months of age, although it can also occur in older children. Individuals with HSES have extremely high body temperatures and multiple organ failures. This condition often causes long term neurological problems or death. The cause of the HSES is unknown. There is no cure for HSES; however, different methods can be used to try to manage associated symptoms.[1208][12105]


Synonyms

  • HSES
  • Hemorrhagic shock and encephalopathy syndrome

For more information, visit GARD.

National Organization for Rare Disorders