This information is provided by the National Institutes of Health (NIH) Genetic and Rare Diseases Information Center (GARD).
IRVAN syndrome is an acronym for “idiopathic retinal vasculitis-aneurysms-neuroretinitis syndrome,” a condition that primarily affects the eyes. Although this condition can occur in people of all ages, it is most commonly diagnosed in the third or fourth decade of life. The severity of the condition varies from person to person with some affected people experiencing a mild form that resolves on its own and others experiencing a severe form that may progress to vitreous hemorrhage (leakage of blood into the eye), vision loss and/or glaucoma. The underlying cause of IRVAN syndrome is currently unknown. Most cases occur sporadically in people with no family history of the condition. Treatment varies based on the severity of the condition and the associated signs and symptoms. In severe cases, surgery or medications such as corticosteroids may be recommended.
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