craniopharyngioma

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Disease Overview

A benign, partly cystic, epithelial tumor of the sellar region, presumably derived from Rathke pouch epithelium. It affects mainly children and young adults. There are two clinicopathological forms: adamantinomatous craniopharyngioma and papillary craniopharyngioma. The most significant factor associated with recurrence is the extent of surgical resection, with lesions greater than 5 cm in diameter carrying a markedly worse prognosis. (Adapted from WHO)


Synonyms

  • Adamantinomatous tumor
  • Adamantinomatous tumour
  • Dysodontogenic epithelial tumor
  • Dysodontogenic epithelial tumour
  • Rathke pouch neoplasm
  • Rathke pouch tumor
  • Rathke pouch tumour
  • Rathke's pouch neoplasm
  • Rathke's pouch tumor
  • Rathke's pouch tumour
  • craniopharyngeal duct tumor
  • craniopharyngeal duct tumour
  • craniopharyngioma (WHO grade I)
  • craniopharyngioma (morphologic abnormality)
  • craniopharyngioma, benign
  • cystoma
  • neoplasm of Rathke's pouch
  • tumor of Rathke's pouch
  • tumour of Rathke's pouch

GARD Disease Summary

The Genetic and Rare Diseases Information Center (GARD) has information and resources for patients, caregivers, and families that may be helpful before and after diagnosis of this condition. GARD is a program of the National Center for Advancing Translational Sciences (NCATS), part of the National Institutes of Health (NIH).

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Orphanet

Orphanet has a summary about this condition that may include information on the diagnosis, care, and treatment as well as other resources. Some of the information and resources are available in languages other than English. The summary may include medical terms, so we encourage you to share and discuss this information with your doctor. Orphanet is the French National Institute for Health and Medical Research and the Health Programme of the European Union.

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National Organization for Rare Disorders