Dubin-Johnson syndrome

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Disease Overview

Dubin-Johnson syndrome (DJS) is a benign, inherited liver disorder characterized clinically by chronic, predominantly conjugated, hyperbilirubinemia and histopathologically by black-brown pigment deposition in parenchymal liver cells.


Synonyms

  • DJS
  • Dubin Johnson Syndrome
  • Dubin Johnson syndrome
  • Dubin-Johnson syndrome
  • Dubin-Sprinz disease
  • Sprinz-Nelson syndrome
  • chronic idiopathic jaundice
  • conjugated hyperbilirubinemia
  • hyperbilirubinemia 2
  • hyperbilirubinemia type 2
  • hyperbilirubinemia, Dubin-Johnson typeDJS
  • Dubin Johnson Syndrome
  • Dubin Johnson syndrome
  • Dubin-Johnson syndrome
  • Dubin-Sprinz disease
  • Sprinz-Nelson syndrome
  • chronic idiopathic jaundice
  • conjugated hyperbilirubinemia
  • hyperbilirubinemia 2
  • hyperbilirubinemia type 2
  • hyperbilirubinemia, Dubin-Johnson type