X-linked lymphoproliferative disease due to XIAP deficiency

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Disease Overview

A condition of decreased or absent presence of baculoviral IAP repeat-containing protein 4. Deficiency of this protein is associated with X-linked lymphoproliferative syndrome 2.


Synonyms

  • X-linked lymphoproliferative disease due to XIAP deficiency
  • X-linked lymphoproliferative syndrome type 2
  • XIAP deficiency
  • XIAP deficiency/XLPs
  • XIAP-related lymphoproliferative disease, X-linked
  • XLP2
  • Xiap deficiency
  • lymphoproliferative syndrome, X-linked, 2
  • lymphoproliferative syndrome, X-linked, 2, X-linked recessive
  • lymphoproliferative syndrome, X-linked, type 2X-linked lymphoproliferative disease due to XIAP deficiency
  • X-linked lymphoproliferative syndrome type 2
  • XIAP deficiency
  • XIAP deficiency/XLPs
  • XIAP-related lymphoproliferative disease, X-linked
  • XLP2
  • Xiap deficiency
  • lymphoproliferative syndrome, X-linked, 2
  • lymphoproliferative syndrome, X-linked, 2, X-linked recessive
  • lymphoproliferative syndrome, X-linked, type 2