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Use the form below to explore NORD's comprehensive rare disease database. Search for detailed information on rare diseases, including NORD's authoritative Rare Disease Reports and data from other reliable sources.
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desmoplastic small round cell tumor

The information provided on this page is for informational purposes only. The National Organization for Rare Disorders (NORD) does not endorse the information presented. The content has been gathered in partnership with the MONDO Disease Ontology. Please consult with a healthcare professional for medical advice and treatment.

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Disease Overview

Desmoplastic small round cell tumor (DSRCT) is an aggressive soft tissue cancer that typically arises in serous lined surfaces of the abdominal or pelvic peritoneum, and spreads to the omentum, lymph nodes and hematogenously disseminates especially to the liver. Extraserous primary location has been reported in exceptional cases.

Synonyms

  • DSRCT
  • Desmoplas. small round cell tumor
  • Desmoplas. small round cell tumour
  • Desmoplastic small round cell tumor
  • Desmoplastic small round cell tumour
  • Desmoplastic small round-cell neoplasm
  • Desmoplastic small round-cell tumor
  • Desmoplastic small round-cell tumour
  • Polyphenotypic small round cell tumor
  • Polyphenotypic small round cell tumour
  • desmoplastic small round cell tumor
  • desmoplastic small-round-cell tumor
  • desmoplastic small-round-cell tumour
GARD Disease Summary

The Genetic and Rare Diseases Information Center (GARD) has information and resources for patients, caregivers, and families that may be helpful before and after diagnosis of this condition. GARD is a program of the National Center for Advancing Translational Sciences (NCATS), part of the National Institutes of Health (NIH).

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Orphanet

Orphanet has a summary about this condition that may include information on the diagnosis, care, and treatment as well as other resources. Some of the information and resources are available in languages other than English. The summary may include medical terms, so we encourage you to share and discuss this information with your doctor. Orphanet is the French National Institute for Health and Medical Research and the Health Programme of the European Union.

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