peeling skin syndrome

Disease Overview

Peeling skin syndrome (PSS) refers to a group of rare autosomal recessive forms of ichthyosis that is characterized clinically by superficial, asymptomatic, spontaneous peeling of the skin and histologically by a shedding of the outer layers of the epidermis. PSS presents with either an acral (acral PSS) or a generalized distribution (generalized PSS type A (non inflammatory) or B (inflammatory)). Some cases remain difficult to classify, suggesting that there could be additional subtypes of PSS.

Synonyms

• PSS
• deciduous skin
• familial continuous skin peeling
• familial continuous skin peeling syndrome
• idiopathic deciduous skin
• keratosis exfoliativa congenita
• peeling skin disease
• skin peeling syndromePSS
• deciduous skin
• familial continuous skin peeling
• familial continuous skin peeling syndrome
• idiopathic deciduous skin
• keratosis exfoliativa congenita
• peeling skin disease
• skin peeling syndrome