rosette-forming glioneuronal tumor of fourth ventricule

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Disease Overview

A central nervous system neoplasm mostly occurring in the fourth ventricle region. It is characterized by the presence of neurocytes forming pseudorosettes and astrocytes which contain Rosenthal fibers. Cytologic atypia is minimal.


Synonyms

  • DNT of the cerebellum
  • RGNT
  • dysembryoplastic neuroepithelial tumor of cerebellum
  • dysembryoplastic neuroepithelial tumour of cerebellum
  • rosette-forming glioneuronal tumor
  • rosette-forming glioneuronal tumour

GARD Disease Summary

The Genetic and Rare Diseases Information Center (GARD) has information and resources for patients, caregivers, and families that may be helpful before and after diagnosis of this condition. GARD is a program of the National Center for Advancing Translational Sciences (NCATS), part of the National Institutes of Health (NIH).

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Orphanet

Orphanet has a summary about this condition that may include information on the diagnosis, care, and treatment as well as other resources. Some of the information and resources are available in languages other than English. The summary may include medical terms, so we encourage you to share and discuss this information with your doctor. Orphanet is the French National Institute for Health and Medical Research and the Health Programme of the European Union.

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