somatostatinoma

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Disease Overview

A rare, usually malignant neuroendocrine tumor arizing from delta cells. This neoplasm produces large amounts of somatostatin, which may result in a syndrome characterized by diarrhea, steatorrhea, weight loss, and gastric hyposecretion. Sixty percent are found in the pancreas and 40% in the duodenum or jejunum. The peak incidence occurs between 40 and 60 years of age; women are affected more than men by 2:1.

Synonyms

Delta cell tumor
Delta cell tumour
Somatomedin-secreting carcinoid
ampullary somatostatinoma
carcinoid somatostatinoma
malignant islet cell tumor
malignant islet cell tumour
somatostatin cell neoplasm
somatostatin cell tumor
somatostatin cell tumour
somatostatin producing tumor
somatostatin producing tumour
somatostatin-producing NET
somatostatin-producing neuroendocrine tumor
somatostatin-producing neuroendocrine tumour
somatostatin-producing tumor
somatostatin-producing tumour
somatostatin-secreting pancreatic neoplasm
somatostatinoma
tumor of Delta cells
tumor of the Delta cells
tumour of Delta cells
tumour of the Delta cells

GARD Disease Summary

The Genetic and Rare Diseases Information Center (GARD) has information and resources for patients, caregivers, and families that may be helpful before and after diagnosis of this condition. GARD is a program of the National Center for Advancing Translational Sciences (NCATS), part of the National Institutes of Health (NIH).

View report

Orphanet

Orphanet has a summary about this condition that may include information on the diagnosis, care, and treatment as well as other resources. Some of the information and resources are available in languages other than English. The summary may include medical terms, so we encourage you to share and discuss this information with your doctor. Orphanet is the French National Institute for Health and Medical Research and the Health Programme of the European Union.