Cutaneous necrotizing vasculitis (CNV) is characterized by inflammation and tissue damage (necrosis) of blood vessel walls (lumen) and associated skin (cutaneous) lesions. CNV may be a primary disease process or occur as a result of, or in association with, a number of different underlying disorders (e.g., certain infections, certain autoimmune disorders) or other factors (e.g., allergic reaction or hypersensitivity to certain medications, toxins, or inhaled environmental irritants). It is important to determine whether there is an underlying disorder that leads to the CNV before treatment is started.
CNV is one of a larger group of disorders involving inflammation and blood vessels known as the vasculitides or the vasculitic syndromes. These syndromes range from modest disorders limited to the skin to more serious ones that may involve various organ systems.
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