Bifid nose

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Disease Overview

A bifid nose is a relatively uncommon malformation that is characterized by the nose being divided into two parts. There is a large degree of variability in the severity of the condition, ranging from a minimally noticeable groove down the center of the nasal tip to a complete clefting of the underlying bones and cartilage, resulting in 2 complete half noses.[3706][3707] It is often associated with hypertelorbitism and midline clefts of the lip.[3706] The airway usually is adequate despite the cosmetic appearance associated with the condition.[3707] Both autosomal recessive and autosomal dominant inheritance of a bifid nose has been observed.[3708] It may also occur with frontonasal dysplasia (a condition in with several possible findings limited to the head and neck), for which several inheritance patterns have been reported.[3709] Treatment typically consists of surgical reconstruction to repair the malformation.[3706]


Synonyms

  • Median fissure of nose
  • Nose, median cleft of

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National Organization for Rare Disorders