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malignant peripheral nerve sheath tumor

The information provided on this page is for informational purposes only. The National Organization for Rare Disorders (NORD) does not endorse the information presented. The content has been gathered in partnership with the MONDO Disease Ontology. Please consult with a healthcare professional for medical advice and treatment.

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Disease Overview

Malignant peripheral nerve sheath tumor (MPNST) is a rare and often aggressive soft tissue sarcoma occurring in a wide range of anatomical sites.


Synonyms

  • MPNST
  • Malig. periph. nerve sheath tum.
  • malignant neoplasm of peripheral nerve sheath
  • malignant neoplasm of the peripheral nerve sheath
  • malignant neurilemmoma
  • malignant neurilemoma
  • malignant neurofibroma
  • malignant peripheral nerve sheath neoplasm
  • malignant peripheral nerve sheath tumor
  • malignant peripheral nerve sheath tumor (morphologic abnormality)
  • malignant peripheral nerve sheath tumor [dup] (morphologic abnormality)
  • malignant peripheral nerve sheath tumour (morphologic abnormality)
  • malignant peripheral nerve sheath tumour [dup] (morphologic abnormality)
  • malignant schwannoma
  • malignant tumor of peripheral nerve sheath
  • malignant tumor of the peripheral nerve sheath
  • malignant tumour of peripheral nerve sheath
  • malignant tumour of the peripheral nerve sheath
  • neurofibrosarcoma
  • neurofibrosarcoma, malignant
  • neurogenic sarcoma
  • schwannoma, malignant

GARD Disease Summary

The Genetic and Rare Diseases Information Center (GARD) has information and resources for patients, caregivers, and families that may be helpful before and after diagnosis of this condition. GARD is a program of the National Center for Advancing Translational Sciences (NCATS), part of the National Institutes of Health (NIH).

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Orphanet

Orphanet has a summary about this condition that may include information on the diagnosis, care, and treatment as well as other resources. Some of the information and resources are available in languages other than English. The summary may include medical terms, so we encourage you to share and discuss this information with your doctor. Orphanet is the French National Institute for Health and Medical Research and the Health Programme of the European Union.

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