otodental syndrome

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Disease Overview

Otodental syndrome is a very rare inherited condition characterized by grossly enlarged canine and molar teeth (globodontia) associated with sensorineural hearing loss.


Synonyms

  • chromosome 11q13 deletion syndrome
  • globodontia
  • oculootodental syndrome
  • otodental dysplasia
  • otodental dysplasia chromosome deletion syndrome
  • otodental syndrome
  • otodental syndrome with colobomachromosome 11q13 deletion syndrome
  • globodontia
  • oculootodental syndrome
  • otodental dysplasia
  • otodental dysplasia chromosome deletion syndrome
  • otodental syndrome
  • otodental syndrome with coloboma