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pancreatic endocrine carcinoma

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Disease Overview

An aggressive, high-grade and poorly differentiated carcinoma with neuroendocrine differentiation that arises from the pancreas. The mitotic count is more than 20 per 10 HPF. According to the size of the malignant cells, the prominence of the nucleoli, and the amount of cytoplasm, it is classified either as small or large cell neuroendocrine carcinoma.


Synonyms

  • Pancreatic Neuroendocrine cancer
  • carcinoma of endocrine pancreas
  • carcinoma, islet cell, malignant
  • endocrine pancreas carcinoma
  • high grade pancreatic neuroendocrine carcinoma
  • high-grade pancreatic neuroendocrine carcinoma
  • islet cell cancer
  • islet cell carcinoma
  • islet cell carcinoma (morphologic abnormality)
  • malignant islet cell tumor
  • malignant islet cell tumour
  • malignant neoplasm of islets of Langerhans
  • malignant pancreatic endocrine tumor
  • malignant pancreatic endocrine tumour
  • neuroendocrine carcinoma of pancreas
  • pancreatic NEC
  • pancreatic NEC G3
  • pancreatic endocrine cancer
  • pancreatic endocrine carcinoma
  • pancreatic neuroendocrine carcinoma
  • poorly differentiated pancreatic endocrine carcinoma
  • poorly-differentiated NEN of pancreas
  • poorly-differentiated neuroendocrine neoplasm of pancreas
  • poorly-differentiated pancreatic NEN
  • poorly-differentiated pancreatic neuroendocrine neoplasm

GARD Disease Summary

The Genetic and Rare Diseases Information Center (GARD) has information and resources for patients, caregivers, and families that may be helpful before and after diagnosis of this condition. GARD is a program of the National Center for Advancing Translational Sciences (NCATS), part of the National Institutes of Health (NIH).

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Orphanet

Orphanet has a summary about this condition that may include information on the diagnosis, care, and treatment as well as other resources. Some of the information and resources are available in languages other than English. The summary may include medical terms, so we encourage you to share and discuss this information with your doctor. Orphanet is the French National Institute for Health and Medical Research and the Health Programme of the European Union.

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